ACADS (acyl-Coenzyme A dehydrogenase)，is a homotetrameric mitochondrial flavoprotein that belongs to the acyl-CoA dehydrogenase family. This enzyme catalyzes the initial step of the mitochondrial fatty acid beta-oxidation pathway. Mutation of this gene causes SCAD deficiency an acute acidosis and muscle weakness in infants and lipid-storage myopathy in adults.
應用類型
Western Blot analysis (1-4 μg/ml).
免疫原
Synthetic peptide surrounding amino acid 380 of rat ACADS
來源宿主
兔
反應性
經檢測驗證，可與人、小鼠、大鼠種屬來源的ACADS蛋白發生免疫反應.
保存建議
提供的ACADS抗體為無色溶液形式，產品濃度為0.5 mg/ml，溶解于包含有30%甘油, 0.5% BSA, 5 mM EDTA和0.01%硫柳汞的PBS緩沖液（pH 7.2）中.請在收到該ACADS抗體產品后，將其置于-20 °C冷凍保存，建議分裝使用以避免反復凍融.
